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Resource ValueSet/FHIR Server from package us.nlm.vsac#0.21.0 (219 ms)

Package us.nlm.vsac
Type ValueSet
Id Id
FHIR Version R4
Source http://fhir.org/packages/us.nlm.vsac/https://vsac.nlm.nih.gov/valueset/2.16.840.1.113883.3.464.1003.120.11.1003/expansion
Url http://cts.nlm.nih.gov/fhir/ValueSet/2.16.840.1.113883.3.464.1003.120.11.1003
Version 20240206
Status active
Date 2024-02-06T01:09:28-05:00
Name DisordersOfTheImmuneSystem
Title Disorders of the Immune System
Experimental False
Realm us
Authority hl7
Purpose (Clinical Focus: The purpose of this value set is to represent concepts for a diagnosis of conditions affecting the immune system.),(Data Element Scope: This value set may use a model element related to Diagnosis.),(Inclusion Criteria: Includes concepts that represent a diagnosis of disorders of the immune system including disorders of the immunoglobulins and the complement system.),(Exclusion Criteria: No exclusions.)

Resources that use this resource

ValueSet
http://cts.nlm.nih.gov/fhir/ValueSet/2.16.840.1.113883.3.464.1003.120.12.1001 Disorders of the Immune System

Resources that this resource uses

CodeSystem
http://hl7.org/fhir/sid/icd-10-cm International Classification of Diseases, 10th Revision, Clinical Modification (ICD-10-CM)
http://hl7.org/fhir/sid/icd-10-cm International Classification of Diseases, 10th Revision, Clinical Modification (ICD-10-CM)


Source

{
  "resourceType" : "ValueSet",
  "id" : "2.16.840.1.113883.3.464.1003.120.11.1003",
  "meta" : {
    "versionId" : "35",
    "lastUpdated" : "2024-02-06T01:09:28.000-05:00",
    "profile" : [
      "http://hl7.org/fhir/StructureDefinition/shareablevalueset",
      "http://hl7.org/fhir/us/cqfmeasures/StructureDefinition/computable-valueset-cqfm",
      "http://hl7.org/fhir/us/cqfmeasures/StructureDefinition/publishable-valueset-cqfm"
    ]
  },
  "extension" : [
    {
      "url" : "http://hl7.org/fhir/StructureDefinition/valueset-author",
      "valueContactDetail" : {
        "name" : "NCQA PHEMUR Author"
      }
    },
    {
      "url" : "http://hl7.org/fhir/StructureDefinition/resource-lastReviewDate",
      "valueDate" : "2024-02-06"
    },
    {
      "url" : "http://hl7.org/fhir/StructureDefinition/valueset-effectiveDate",
      "valueDate" : "2024-02-06"
    }
  ],
  "url" : "http://cts.nlm.nih.gov/fhir/ValueSet/2.16.840.1.113883.3.464.1003.120.11.1003",
  "identifier" : [
    {
      "system" : "urn:ietf:rfc:3986",
      "value" : "urn:oid:2.16.840.1.113883.3.464.1003.120.11.1003"
    }
  ],
  "version" : "20240206",
  "name" : "DisordersOfTheImmuneSystem",
  "title" : "Disorders of the Immune System",
  "status" : "active",
  "date" : "2024-02-06T01:09:28-05:00",
  "publisher" : "NCQA PHEMUR",
  "jurisdiction" : [
    {
      "coding" : [
        {
          "system" : "urn:iso:std:iso:3166",
          "code" : "US"
        }
      ]
    }
  ],
  "purpose" : "(Clinical Focus: The purpose of this value set is to represent concepts for a diagnosis of conditions affecting the immune system.),(Data Element Scope: This value set may use a model element related to Diagnosis.),(Inclusion Criteria: Includes concepts that represent a diagnosis of disorders of the immune system including disorders of the immunoglobulins and the complement system.),(Exclusion Criteria: No exclusions.)",
  "compose" : {
    "include" : [
      {
        "system" : "http://hl7.org/fhir/sid/icd-10-cm",
        "concept" : [
          {
            "code" : "D80.0",
            "display" : "Hereditary hypogammaglobulinemia"
          },
          {
            "code" : "D80.1",
            "display" : "Nonfamilial hypogammaglobulinemia"
          },
          {
            "code" : "D80.2",
            "display" : "Selective deficiency of immunoglobulin A [IgA]"
          },
          {
            "code" : "D80.3",
            "display" : "Selective deficiency of immunoglobulin G [IgG] subclasses"
          },
          {
            "code" : "D80.4",
            "display" : "Selective deficiency of immunoglobulin M [IgM]"
          },
          {
            "code" : "D80.5",
            "display" : "Immunodeficiency with increased immunoglobulin M [IgM]"
          },
          {
            "code" : "D80.6",
            "display" : "Antibody deficiency with near-normal immunoglobulins or with hyperimmunoglobulinemia"
          },
          {
            "code" : "D80.7",
            "display" : "Transient hypogammaglobulinemia of infancy"
          },
          {
            "code" : "D80.8",
            "display" : "Other immunodeficiencies with predominantly antibody defects"
          },
          {
            "code" : "D80.9",
            "display" : "Immunodeficiency with predominantly antibody defects, unspecified"
          },
          {
            "code" : "D81.0",
            "display" : "Severe combined immunodeficiency [SCID] with reticular dysgenesis"
          },
          {
            "code" : "D81.1",
            "display" : "Severe combined immunodeficiency [SCID] with low T- and B-cell numbers"
          },
          {
            "code" : "D81.2",
            "display" : "Severe combined immunodeficiency [SCID] with low or normal B-cell numbers"
          },
          {
            "code" : "D81.4",
            "display" : "Nezelof's syndrome"
          },
          {
            "code" : "D81.6",
            "display" : "Major histocompatibility complex class I deficiency"
          },
          {
            "code" : "D81.7",
            "display" : "Major histocompatibility complex class II deficiency"
          },
          {
            "code" : "D81.82",
            "display" : "Activated Phosphoinositide 3-kinase Delta Syndrome [APDS]"
          },
          {
            "code" : "D81.89",
            "display" : "Other combined immunodeficiencies"
          },
          {
            "code" : "D81.9",
            "display" : "Combined immunodeficiency, unspecified"
          },
          {
            "code" : "D82.0",
            "display" : "Wiskott-Aldrich syndrome"
          },
          {
            "code" : "D82.1",
            "display" : "Di George's syndrome"
          },
          {
            "code" : "D82.2",
            "display" : "Immunodeficiency with short-limbed stature"
          },
          {
            "code" : "D82.3",
            "display" : "Immunodeficiency following hereditary defective response to Epstein-Barr virus"
          },
          {
            "code" : "D82.4",
            "display" : "Hyperimmunoglobulin E [IgE] syndrome"
          },
          {
            "code" : "D82.8",
            "display" : "Immunodeficiency associated with other specified major defects"
          },
          {
            "code" : "D82.9",
            "display" : "Immunodeficiency associated with major defect, unspecified"
          },
          {
            "code" : "D83.0",
            "display" : "Common variable immunodeficiency with predominant abnormalities of B-cell numbers and function"
          },
          {
            "code" : "D83.1",
            "display" : "Common variable immunodeficiency with predominant immunoregulatory T-cell disorders"
          },
          {
            "code" : "D83.2",
            "display" : "Common variable immunodeficiency with autoantibodies to B- or T-cells"
          },
          {
            "code" : "D83.8",
            "display" : "Other common variable immunodeficiencies"
          },
          {
            "code" : "D83.9",
            "display" : "Common variable immunodeficiency, unspecified"
          },
          {
            "code" : "D84.0",
            "display" : "Lymphocyte function antigen-1 [LFA-1] defect"
          },
          {
            "code" : "D84.1",
            "display" : "Defects in the complement system"
          },
          {
            "code" : "D84.81",
            "display" : "Immunodeficiency due to conditions classified elsewhere"
          },
          {
            "code" : "D84.821",
            "display" : "Immunodeficiency due to drugs"
          },
          {
            "code" : "D84.822",
            "display" : "Immunodeficiency due to external causes"
          },
          {
            "code" : "D84.89",
            "display" : "Other immunodeficiencies"
          },
          {
            "code" : "D84.9",
            "display" : "Immunodeficiency, unspecified"
          },
          {
            "code" : "D89.3",
            "display" : "Immune reconstitution syndrome"
          },
          {
            "code" : "D89.810",
            "display" : "Acute graft-versus-host disease"
          },
          {
            "code" : "D89.811",
            "display" : "Chronic graft-versus-host disease"
          },
          {
            "code" : "D89.812",
            "display" : "Acute on chronic graft-versus-host disease"
          },
          {
            "code" : "D89.813",
            "display" : "Graft-versus-host disease, unspecified"
          },
          {
            "code" : "D89.82",
            "display" : "Autoimmune lymphoproliferative syndrome [ALPS]"
          },
          {
            "code" : "D89.831",
            "display" : "Cytokine release syndrome, grade 1"
          },
          {
            "code" : "D89.832",
            "display" : "Cytokine release syndrome, grade 2"
          },
          {
            "code" : "D89.833",
            "display" : "Cytokine release syndrome, grade 3"
          },
          {
            "code" : "D89.834",
            "display" : "Cytokine release syndrome, grade 4"
          },
          {
            "code" : "D89.835",
            "display" : "Cytokine release syndrome, grade 5"
          },
          {
            "code" : "D89.839",
            "display" : "Cytokine release syndrome, grade unspecified"
          },
          {
            "code" : "D89.84",
            "display" : "IgG4-related disease"
          },
          {
            "code" : "D89.89",
            "display" : "Other specified disorders involving the immune mechanism, not elsewhere classified"
          },
          {
            "code" : "D89.9",
            "display" : "Disorder involving the immune mechanism, unspecified"
          }
        ]
      }
    ]
  },
  "expansion" : {
    "identifier" : "urn:uuid:df1c3712-24c5-4122-9ca6-7ca5db7c73fb",
    "timestamp" : "2024-12-10T10:44:31-05:00",
    "total" : 53,
    "contains" : [
      {
        "system" : "http://hl7.org/fhir/sid/icd-10-cm",
        "version" : "2025",
        "code" : "D80.0",
        "display" : "Hereditary hypogammaglobulinemia"
      },
      {
        "system" : "http://hl7.org/fhir/sid/icd-10-cm",
        "version" : "2025",
        "code" : "D80.1",
        "display" : "Nonfamilial hypogammaglobulinemia"
      },
      {
        "system" : "http://hl7.org/fhir/sid/icd-10-cm",
        "version" : "2025",
        "code" : "D80.2",
        "display" : "Selective deficiency of immunoglobulin A [IgA]"
      },
      {
        "system" : "http://hl7.org/fhir/sid/icd-10-cm",
        "version" : "2025",
        "code" : "D80.3",
        "display" : "Selective deficiency of immunoglobulin G [IgG] subclasses"
      },
      {
        "system" : "http://hl7.org/fhir/sid/icd-10-cm",
        "version" : "2025",
        "code" : "D80.4",
        "display" : "Selective deficiency of immunoglobulin M [IgM]"
      },
      {
        "system" : "http://hl7.org/fhir/sid/icd-10-cm",
        "version" : "2025",
        "code" : "D80.5",
        "display" : "Immunodeficiency with increased immunoglobulin M [IgM]"
      },
      {
        "system" : "http://hl7.org/fhir/sid/icd-10-cm",
        "version" : "2025",
        "code" : "D80.6",
        "display" : "Antibody deficiency with near-normal immunoglobulins or with hyperimmunoglobulinemia"
      },
      {
        "system" : "http://hl7.org/fhir/sid/icd-10-cm",
        "version" : "2025",
        "code" : "D80.7",
        "display" : "Transient hypogammaglobulinemia of infancy"
      },
      {
        "system" : "http://hl7.org/fhir/sid/icd-10-cm",
        "version" : "2025",
        "code" : "D80.8",
        "display" : "Other immunodeficiencies with predominantly antibody defects"
      },
      {
        "system" : "http://hl7.org/fhir/sid/icd-10-cm",
        "version" : "2025",
        "code" : "D80.9",
        "display" : "Immunodeficiency with predominantly antibody defects, unspecified"
      },
      {
        "system" : "http://hl7.org/fhir/sid/icd-10-cm",
        "version" : "2025",
        "code" : "D81.0",
        "display" : "Severe combined immunodeficiency [SCID] with reticular dysgenesis"
      },
      {
        "system" : "http://hl7.org/fhir/sid/icd-10-cm",
        "version" : "2025",
        "code" : "D81.1",
        "display" : "Severe combined immunodeficiency [SCID] with low T- and B-cell numbers"
      },
      {
        "system" : "http://hl7.org/fhir/sid/icd-10-cm",
        "version" : "2025",
        "code" : "D81.2",
        "display" : "Severe combined immunodeficiency [SCID] with low or normal B-cell numbers"
      },
      {
        "system" : "http://hl7.org/fhir/sid/icd-10-cm",
        "version" : "2025",
        "code" : "D81.4",
        "display" : "Nezelof's syndrome"
      },
      {
        "system" : "http://hl7.org/fhir/sid/icd-10-cm",
        "version" : "2025",
        "code" : "D81.6",
        "display" : "Major histocompatibility complex class I deficiency"
      },
      {
        "system" : "http://hl7.org/fhir/sid/icd-10-cm",
        "version" : "2025",
        "code" : "D81.7",
        "display" : "Major histocompatibility complex class II deficiency"
      },
      {
        "system" : "http://hl7.org/fhir/sid/icd-10-cm",
        "version" : "2025",
        "code" : "D81.82",
        "display" : "Activated Phosphoinositide 3-kinase Delta Syndrome [APDS]"
      },
      {
        "system" : "http://hl7.org/fhir/sid/icd-10-cm",
        "version" : "2025",
        "code" : "D81.89",
        "display" : "Other combined immunodeficiencies"
      },
      {
        "system" : "http://hl7.org/fhir/sid/icd-10-cm",
        "version" : "2025",
        "code" : "D81.9",
        "display" : "Combined immunodeficiency, unspecified"
      },
      {
        "system" : "http://hl7.org/fhir/sid/icd-10-cm",
        "version" : "2025",
        "code" : "D82.0",
        "display" : "Wiskott-Aldrich syndrome"
      },
      {
        "system" : "http://hl7.org/fhir/sid/icd-10-cm",
        "version" : "2025",
        "code" : "D82.1",
        "display" : "Di George's syndrome"
      },
      {
        "system" : "http://hl7.org/fhir/sid/icd-10-cm",
        "version" : "2025",
        "code" : "D82.2",
        "display" : "Immunodeficiency with short-limbed stature"
      },
      {
        "system" : "http://hl7.org/fhir/sid/icd-10-cm",
        "version" : "2025",
        "code" : "D82.3",
        "display" : "Immunodeficiency following hereditary defective response to Epstein-Barr virus"
      },
      {
        "system" : "http://hl7.org/fhir/sid/icd-10-cm",
        "version" : "2025",
        "code" : "D82.4",
        "display" : "Hyperimmunoglobulin E [IgE] syndrome"
      },
      {
        "system" : "http://hl7.org/fhir/sid/icd-10-cm",
        "version" : "2025",
        "code" : "D82.8",
        "display" : "Immunodeficiency associated with other specified major defects"
      },
      {
        "system" : "http://hl7.org/fhir/sid/icd-10-cm",
        "version" : "2025",
        "code" : "D82.9",
        "display" : "Immunodeficiency associated with major defect, unspecified"
      },
      {
        "system" : "http://hl7.org/fhir/sid/icd-10-cm",
        "version" : "2025",
        "code" : "D83.0",
        "display" : "Common variable immunodeficiency with predominant abnormalities of B-cell numbers and function"
      },
      {
        "system" : "http://hl7.org/fhir/sid/icd-10-cm",
        "version" : "2025",
        "code" : "D83.1",
        "display" : "Common variable immunodeficiency with predominant immunoregulatory T-cell disorders"
      },
      {
        "system" : "http://hl7.org/fhir/sid/icd-10-cm",
        "version" : "2025",
        "code" : "D83.2",
        "display" : "Common variable immunodeficiency with autoantibodies to B- or T-cells"
      },
      {
        "system" : "http://hl7.org/fhir/sid/icd-10-cm",
        "version" : "2025",
        "code" : "D83.8",
        "display" : "Other common variable immunodeficiencies"
      },
      {
        "system" : "http://hl7.org/fhir/sid/icd-10-cm",
        "version" : "2025",
        "code" : "D83.9",
        "display" : "Common variable immunodeficiency, unspecified"
      },
      {
        "system" : "http://hl7.org/fhir/sid/icd-10-cm",
        "version" : "2025",
        "code" : "D84.0",
        "display" : "Lymphocyte function antigen-1 [LFA-1] defect"
      },
      {
        "system" : "http://hl7.org/fhir/sid/icd-10-cm",
        "version" : "2025",
        "code" : "D84.1",
        "display" : "Defects in the complement system"
      },
      {
        "system" : "http://hl7.org/fhir/sid/icd-10-cm",
        "version" : "2025",
        "code" : "D84.81",
        "display" : "Immunodeficiency due to conditions classified elsewhere"
      },
      {
        "system" : "http://hl7.org/fhir/sid/icd-10-cm",
        "version" : "2025",
        "code" : "D84.821",
        "display" : "Immunodeficiency due to drugs"
      },
      {
        "system" : "http://hl7.org/fhir/sid/icd-10-cm",
        "version" : "2025",
        "code" : "D84.822",
        "display" : "Immunodeficiency due to external causes"
      },
      {
        "system" : "http://hl7.org/fhir/sid/icd-10-cm",
        "version" : "2025",
        "code" : "D84.89",
        "display" : "Other immunodeficiencies"
      },
      {
        "system" : "http://hl7.org/fhir/sid/icd-10-cm",
        "version" : "2025",
        "code" : "D84.9",
        "display" : "Immunodeficiency, unspecified"
      },
      {
        "system" : "http://hl7.org/fhir/sid/icd-10-cm",
        "version" : "2025",
        "code" : "D89.3",
        "display" : "Immune reconstitution syndrome"
      },
      {
        "system" : "http://hl7.org/fhir/sid/icd-10-cm",
        "version" : "2025",
        "code" : "D89.810",
        "display" : "Acute graft-versus-host disease"
      },
      {
        "system" : "http://hl7.org/fhir/sid/icd-10-cm",
        "version" : "2025",
        "code" : "D89.811",
        "display" : "Chronic graft-versus-host disease"
      },
      {
        "system" : "http://hl7.org/fhir/sid/icd-10-cm",
        "version" : "2025",
        "code" : "D89.812",
        "display" : "Acute on chronic graft-versus-host disease"
      },
      {
        "system" : "http://hl7.org/fhir/sid/icd-10-cm",
        "version" : "2025",
        "code" : "D89.813",
        "display" : "Graft-versus-host disease, unspecified"
      },
      {
        "system" : "http://hl7.org/fhir/sid/icd-10-cm",
        "version" : "2025",
        "code" : "D89.82",
        "display" : "Autoimmune lymphoproliferative syndrome [ALPS]"
      },
      {
        "system" : "http://hl7.org/fhir/sid/icd-10-cm",
        "version" : "2025",
        "code" : "D89.831",
        "display" : "Cytokine release syndrome, grade 1"
      },
      {
        "system" : "http://hl7.org/fhir/sid/icd-10-cm",
        "version" : "2025",
        "code" : "D89.832",
        "display" : "Cytokine release syndrome, grade 2"
      },
      {
        "system" : "http://hl7.org/fhir/sid/icd-10-cm",
        "version" : "2025",
        "code" : "D89.833",
        "display" : "Cytokine release syndrome, grade 3"
      },
      {
        "system" : "http://hl7.org/fhir/sid/icd-10-cm",
        "version" : "2025",
        "code" : "D89.834",
        "display" : "Cytokine release syndrome, grade 4"
      },
      {
        "system" : "http://hl7.org/fhir/sid/icd-10-cm",
        "version" : "2025",
        "code" : "D89.835",
        "display" : "Cytokine release syndrome, grade 5"
      },
      {
        "system" : "http://hl7.org/fhir/sid/icd-10-cm",
        "version" : "2025",
        "code" : "D89.839",
        "display" : "Cytokine release syndrome, grade unspecified"
      },
      {
        "system" : "http://hl7.org/fhir/sid/icd-10-cm",
        "version" : "2025",
        "code" : "D89.84",
        "display" : "IgG4-related disease"
      },
      {
        "system" : "http://hl7.org/fhir/sid/icd-10-cm",
        "version" : "2025",
        "code" : "D89.89",
        "display" : "Other specified disorders involving the immune mechanism, not elsewhere classified"
      },
      {
        "system" : "http://hl7.org/fhir/sid/icd-10-cm",
        "version" : "2025",
        "code" : "D89.9",
        "display" : "Disorder involving the immune mechanism, unspecified"
      }
    ]
  },
  "text" : {
  }
}

XIG built as of ??metadata-date??. Found ??metadata-resources?? resources in ??metadata-packages?? packages.